Primary intestinal lymphangiectasia with lymphedema of lower extremities

Primary intestinal lymphangiectasia (PIL), also known as Waldmann’s disease, is a rare disorder manifested by the presence of dilated lymphatic ducts and leading to protein-losing enteropathy. PIL usually presents early in childhood; however, rarely may be diagnosed adults. Suggestive laboratory findings include hypoproteinemia, hypoalbuminemia, hypogammaglobulinemia. Peripheral pitting edema due hypoalbuminemia main clinical feature. lymphedema less common symptom. We present case 23-year-old woman with lower extremities childhood.